Patent · US Active

AAV-mediated gene therapy for maple syrup urine disease (MSUD)

US12398378B2 · kind B2 · utility

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Key dates

Filing dateApr 10, 2020
Grant dateAug 26, 2025
Priority date
Expiry dateNov 28, 2042

Classification

  • Technology area (CPC C)Chemistry; Metallurgy
  • CPC primaryC12N9/0008
  • WIPO fieldPharmaceuticals
  • WIPO sectorChemistry

Abstract

In some aspects the disclosure provides compositions and methods for promoting expression of functional BCKDHA protein, which is the E1-alpha subunit of the branched-chain alpha-keto acid (BCAA) dehydrogenase complex, in a subject. In some aspects the disclosure provides compositions and methods for promoting expression of functional BCKDHB protein, which is the E1-beta subunit of the branched-chain alpha-keto acid (BCAA) dehydrogenase complex, in a subject. In some aspects the disclosure provides compositions and methods for promoting expression of functional BCKDHA and BCKDHB proteins, in a subject. In some embodiments, the disclosure provides methods of treating a subject having Maple Syrup Urine Disease (MSUD).

Source: USPTO / EPO open patent data. Objective bibliographic and citation counts.